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Semaphorin 4A Mediates Inflammation Resistance of Myeloid-Biased HSC

Dorsa Toghani1, Elmir Mahammadov2, Negar Seyehassatehrani3 , Antonio Scialdone2, Joel Spencer3 and Lev Silberstein1

1Fred Hutchinson Cancer Center, Seattle, WA, USA,

2Helmholtz Institute for Epigenetics, Munich, Germany,

3University of California Merced, CA, USA

Background: Inflammation significantly impairs hematopoietic stem cell (HSC) self-renewal. Despite this, HSC maintain regenerative capacity throughout life suggesting that they are relatively resistant to inflammation-induced damage. However, very few HSC “inflammation resistance” signals are currently known. This represents an important hurdle for understanding not only normal hematopoietic regeneration but also leukemogenesis, since overactivation of normal inflammation resistance pathways has been suggested as a potential mechanism for pre-malignant clonal expansion and survival of AML blasts.

Aims: In the current study, we aimed to define a role of a newly-defined niche factor, Semaphorin 4A (Sema4A), in conferring HSC resistance to acute and chronic inflammation. Further, we sought to understand the molecular events downstream of Sema4A signaling and explore recombinant Sema4A as an HSC-protective molecule in the setting of acute inflammatory stress.

Methods: We utilized mice with germline and conditional deletion of Sema4A and recombinant Sema4A-Fc protein, in conjunction with models of acute inflammatory stress, aging and transplantation. In order to identify underlying cellular and molecular mechanisms, we performed intravital imaging, as well as bulk and single cell RNA-sequencing studies.

Results: We discovered that Sema4A controls HSC dormancy. Unexpectedly, we found that this property of Sema4A is restricted to myeloid-biased HSC (myHSC) an HSC subset which plays a key role in inflammatory response and aging. We found that following acute lipopolysaccharide (LPS)-induced inflammatory stress, Sema4AKO myHSC failed to adequately expand and generated fewer numbers of downstream myeloid progeny. Although the impact of Sema4A absence in this setting was reversible, chronic inflammatory exposure, as exemplified by aging, led to a complete loss of myHSC self-renewal potential and capacity for reconstitution. Transcriptomic studies in both settings revealed that the absence of Sema4A was associated with hyperactivated inflammatory signaling and premature myeloid differentiation, thus identifying this molecule as a key inflammation resistance signal.

Transplantation studies demonstrated that the cellular source of Sema4A is non cell-autonomous, since we observed that while conditional Sema4A deletion from myHSC was functionally inconsequential, 50% of Sema4AKO animals transplanted with WT myHSC died between days 11-20 post-transplant. Intravital imaging revealed markedly enhanced early proliferation of transplanted WT myHSC in Sema4AKO, consistent with the lack of dormancy-inducing effect of Sema4A causing impaired self-renewal and engraftment failure in a highly. Importantly, systemic administration of Sema4A-Fc protein protected myHSC from acute inflammatory injury, as evidenced by improved colony-forming capacity and significantly higher levels of reconstitution post-transplant by myHSC from the mice which we pre-treated with recombinant Sema4A-Fc protein prior to LPS-induced acute inflammatory exposure.

Conclusion: Our results highlight a crucial role of Sema4A-mediated inflammation resistance for preservation of myHSC short- and long-term regenerative function. Interestingly, we observed that both Sema4A and its putative receptor, PlxnD1, are overexpressed in AML blasts as compared to normal bone marrow, and that higher expression of PlxnD1 in AML blasts is associated with a significantly worse survival. This suggests that hyperactivation of Sema4A-PlxnD1 inflammation resistance pathway may promote leukemogenesis and chemoresistance in myeloid malignancies, which will be addressed by our future studies.


Speakers

Lev Silberstein

Fred Hutchinson Cancer Center